Temper Outbursts in Lowe Syndrome: Characteristics, Sequence, Environmental Context and Comparison to Prader-Willi Syndrome

Autor/inn/en	Cressey, Helen; Oliver, Chris; Crawford, Hayley; Waite, Jane
Titel	Temper Outbursts in Lowe Syndrome: Characteristics, Sequence, Environmental Context and Comparison to Prader-Willi Syndrome
Quelle	In: Journal of Applied Research in Intellectual Disabilities, 32 (2019) 5, S.1216-1227 (12 Seiten)Infoseite zur Zeitschrift PDF als Volltext Verfügbarkeit
Zusatzinformation	ORCID (Cressey, Helen) ORCID (Oliver, Chris) ORCID (Crawford, Hayley) ORCID (Waite, Jane)
Sprache	englisch
Dokumenttyp	gedruckt; online; Zeitschriftenaufsatz
ISSN	1360-2322
DOI	10.1111/jar.12613
Schlagwörter	Psychological Patterns; Intellectual Disability; Environmental Influences; Phenomenology; Genetic Disorders; Symptoms (Individual Disorders); Caregiver Attitudes; Children; Aggression; Vandalism; Behavior Patterns; Goal Orientation + Suchen Sie Ihr Suchwort? Intellect; Disability; Disabilities; Verstand; Behinderung; Environmental influence; Umwelteinfluss; Phenomenological psychology; Phänomenologie; Psychologie; Psychiatrische Symptomatik; Child; Kind; Kinder; Zielorientierung; Zielvorstellung
Abstract	Background: There is limited research into the nature and aetiology of temper outbursts in people with intellectual disabilities. In this study, we describe the phenomenology and environmental context of temper outbursts in Lowe syndrome, a rare genetic syndrome in which outbursts are purportedly frequent. Method: A temper outburst interview (TOI) was conducted with caregivers of seventeen individuals with Lowe syndrome to generate an account of the behavioural sequence, common antecedents and consequences of temper outbursts, and to enable comparisons with similar work on Prader-Willi syndrome. Results: Outbursts in Lowe syndrome were frequently triggered by thwarted goal-directed behaviour and were associated with high levels of physical aggression and property destruction. Conclusions: Form and sequence of outbursts showed similarities to Prader-Willi syndrome and to behaviours reported in literature on typically developing children. The results highlight the importance of considering shared aetiology as well as syndrome-specific pathways in the development of outbursts. (As Provided).
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Erfasst von	ERIC (Education Resources Information Center), Washington, DC
Update	2020/1/01