Adapting the Mullen Scales of Early Learning for a Standardized Measure of Development in Children with Rett Syndrome

Autor/inn/en	Clarkson, Tessa; LeBlanc, Jocelyn; DeGregorio, Geneva; Vogel-Farley, Vanessa; Barnes, Katherine; Kaufmann, Walter E.; Nelson, Charles A.
Titel	Adapting the Mullen Scales of Early Learning for a Standardized Measure of Development in Children with Rett Syndrome
Quelle	In: Intellectual and Developmental Disabilities, 55 (2017) 6, S.419-431 (16 Seiten)Infoseite zur Zeitschrift PDF als Volltext Verfügbarkeit
Sprache	englisch
Dokumenttyp	gedruckt; online; Zeitschriftenaufsatz
ISSN	1934-9491
Schlagwörter	Cognitive Ability; Motor Development; Children; Genetic Disorders; Neurological Impairments; Females; Adjustment (to Environment); Behavior Rating Scales; Eye Movements; Visual Perception; Receptive Language; Correlation; Mullen Scales of Early Learning; Vineland Adaptive Behavior Scales + Suchen Sie Ihr Suchwort? Denkfähigkeit; Motorische Entwicklung; Child; Kind; Kinder; Neurodegenerative Erkrankung; Weibliches Geschlecht; Augenbewegung; Visuelle Wahrnehmung; Rezeptive Kommunikationsfähigkeit; Korrelation
Abstract	Rett Syndrome (RTT) is characterized by severe impairment in fine motor (FM) and expressive language (EL) function, making accurate evaluations of development difficult with standardized assessments. In this study, the administration and scoring of the Mullen Scales of Early Learning (MSEL) were adapted to eliminate the confounding effects of FM and EL impairments in assessing development. Forty-seven girls with RTT were assessed with the Adapted-MSEL (MSEL-A), a subset (n = 30) was also assessed using the Vineland Adaptive Behavior Scales-Second Edition (Vineland-II) and a further subset (n = 17) was assessed using an eye-tracking version of the MSEL (MSEL-ET). Participants performed better on the visual reception (VR) and receptive language (RL) domains compared to the FM and EL domains on the MSEL-A. Individual performance on each domain was independent of other domains. Corresponding MSEL-A and Vineland-II domains were significantly correlated. The MSEL-ET was as accurate as the MSEL-A in assessing VR and RL, yet took a 44% less time. Results suggested that the MSEL-A and the MSEL-ET could be viable measures for accurately assessing developmental domains in children with RTT. (As Provided).
Anmerkungen	American Association on Intellectual and Developmental Disabilities. P.O. Box 1897, Lawrence, KS 66044-1897. Tel: 785-843-1235; Fax: 785-843-1274; e-mail: AJMR@allenpress.com; Web site: http://www.aaiddjournals.org/
Erfasst von	ERIC (Education Resources Information Center), Washington, DC
Update	2020/1/01